Aleo, Serena J; Del Dotto, Valentina; Fogazza, Mario; Maresca, Alessandra; Lodi, Tiziana; Goffrini, Paola; Ghelli, Anna; Rugolo, Michela; Carelli, Valerio; Baruffini, Enrico; Zanna, Claudia, Drug repositioning as a therapeutic strategy for neurodegenerations associated with OPA1 mutations, «HUMAN MOLECULAR GENETICS», 2020, 29, pp. 3631 - 3645 [articolo]Open Access
Perli, Elena; Pisano, Annalinda; Pignataro, Maria Gemma; Campese, Antonio Francesco; Pelullo, Maria; Genovese, Ilaria; de Turris, Valeria; Ghelli, Anna Maria; Cerbelli, Bruna; Giordano, Carla; Colotti, Gianni; Morea, Veronica; d'Amati, Giulia, Exogenous peptides are able to penetrate human cell and mitochondrial membranes, stabilize mitochondrial tRNA structures, and rescue severe mitochondrial defects, «THE FASEB JOURNAL», 2020, 34, pp. 7675 - 7686 [articolo]
Tropeano C.V.; Aleo S.J.; Zanna C.; Roberti M.; Scandiffio L.; Loguercio Polosa P.; Fiori J.; Porru E.; Roda A.; Carelli V.; Steimle S.; Daldal F.; Rugolo M.; Ghelli A., Fine-tuning of the respiratory complexes stability and supercomplexes assembly in cells defective of complex III, «BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS», 2020, 1861, Article number: 148133, pp. 1 - 13 [articolo]Open Access
Barca, Juan Manuel Chao; Fogazza, Mario; Rugolo, Michela; Chupin, Stéphanie; Del Dotto, Valentina; Ghelli, Anna Maria; Carelli, Valerio; Simard, Gilles; Procaccio, Vincent; Bonneau, Dominique; Lenaers, Guy; Reynier, Pascal; Zanna, Claudia, Metabolomics hallmarks OPA1 variants correlating with their in-vitro phenotype and predicting clinical severity, «HUMAN MOLECULAR GENETICS ONLINE», 2020, 29, pp. 1319 - 1329 [articolo]Open Access
Iommarini, L.; Ghelli, A.; Diaz, F., Methods and models for functional studies on mtDNA mutations, in: The Human Mitochondrial Genome: From Basic Biology to Disease, Londra, Elsevier, 2020, pp. 305 - 349 [capitolo di libro]
Malferrari, Marco; Ghelli, Anna*; Roggiani, Francesco; Valenti, Giovanni; Paolucci, Francesco; Rugolo, Michela; Rapino, Stefania, Reactive Oxygen Species Produced by Mutated Mitochondrial Respiratory Chains of Entire Cells Monitored Using Modified Microelectrodes, «CHEMELECTROCHEM», 2019, 6, pp. 627 - 633 [articolo]
Tropeano, Concetta Valentina; Fiori, Jessica; Carelli, Valerio; Caporali, Leonardo; Daldal, Fevzi; Ghelli, Anna Maria; Rugolo, Michela, Complex II phosphorylation is triggered by unbalanced redox homeostasis in cells lacking complex III, «BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS», 2018, 1859, pp. 182 - 190 [articolo]
Strobbe, Daniela; Caporali, Leonardo; Iommarini, Luisa; Maresca, Alessandra; Montopoli, Monica; Martinuzzi, Andrea; Achilli, Alessandro; Olivieri, Anna; Torroni, Antonio; Carelli, Valerio; Ghelli, Anna, Haplogroup J mitogenomes are the most sensitive to the pesticide rotenone: Relevance for human diseases, «NEUROBIOLOGY OF DISEASE», 2018, 114, pp. 129 - 139 [articolo]Open Access
Trevisan, Tatiana; Pendin, Diana; Montagna, Aldo; Bova, Sergio; Ghelli, Anna Maria; Daga, Andrea*, Manipulation of Mitochondria Dynamics Reveals Separate Roles for Form and Function in Mitochondria Distribution, «CELL REPORTS», 2018, 23, pp. 1742 - 1753 [articolo]Open Access
Iommarini, Luisa; Ghelli, Anna; Leone, Giulia; Tropeano, Concetta Valentina; Kurelac, Ivana; Amato, Laura Benedetta; Gasparre, Giuseppe; Porcelli, Anna Maria, Mild phenotypes and proper supercomplex assembly in human cells carrying the homoplasmic m.15557G > A mutation in cytochrome b gene, «HUMAN MUTATION», 2018, 39, pp. 92 - 102 [articolo]
Iommarini, Luisa; Ghelli, Anna; Tropeano, Concetta; Kurelac, Ivana; Leone, Giulia; Vidoni, Sara; Lombes, Anne; Zeviani, Massimo; Gasparre, Giuseppe; Porcelli, Anna, Unravelling the Effects of the Mutation m.3571insC/MT-ND1 on Respiratory Complexes Structural Organization, «INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES», 2018, 19, pp. 764 - 780 [articolo]Open Access
Georg, Birgitte; Ghelli, ANNA MARIA; Giordano, Carla; Ross Cisneros, Fred N.; Sadun, Alfredo A.; Carelli, Valerio; Hannibal, Jens; LA MORGIA, Chiara, Melanopsin-expressing retinal ganglion cells are resistant to cell injury, but not always, «MITOCHONDRION», 2017, 36, pp. 77 - 84 [articolo]
Iommarini, Luisa; Ghelli, Anna; Gasparre, Giuseppe; Porcelli, Anna Maria, Mitochondrial metabolism and energy sensing in tumor progression, «BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS», 2017, 1858, pp. 582 - 590 [articolo]Open Access
Giordano, L; Deceglie, S; D'Adamo, P; Valentino, M L; La Morgia, C; Fracasso, F; Roberti, M; Cappellari, M; Petrosillo, G; Ciaravolo, S; Parente, D; Giordano, C; Maresca, A; Iommarini, L; Del Dotto, V; Ghelli, A M; Salomao, S R; Berezovsky, A; Belfort, R; Sadun, A A; Carelli, V; Loguercio Polosa, P; Cantatore, P, Cigarette toxicity triggers Leber's hereditary optic neuropathy by affecting mtDNA copy number, oxidative phosphorylation and ROS detoxification pathways, «CELL DEATH & DISEASE», 2015, 6, Article number: e2021, pp. 1 - 10 [articolo]Open Access
Ghelli, Anna Maria; Valentina C. Tropeano; Rugolo, Michela, Mitochondrial Respiratory Supercomplexes in Physiology and Diseases, in: Redox Proteins in Supercomplexes and Signalosomes, New York, Ricardo O. Louro; Irene Diaz-Moreno, 2015, pp. 149 - 165 [capitolo di libro]